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Konjenital Lober Amfizem [Respir Case Rep]
Respir Case Rep. 2018; 7(1): 50-53 | DOI: 10.5505/respircase.2018.55707

Konjenital Lober Amfizem

Pnar Mutlu, Merve Ilcn Guven
anakkale 18 Mart niversitesi Tp Fakltesi Gs Hastalklar Anabilim Dal, anakkale

Bir ya da birden fazla akcier lobunun dardan bir bas olmadan hiperinflasyonu konjenital lober amfizem olarak tanmlanr. 20.000 ila 30.000 doumda bir izlenen ok nadir bir durumdur. Olgularn %50sinde etyoloji bilinmemektedir. Etyolojide sulanan dier nedenler, broniyal anormallikler ya da alveolar defektlerdir. Yetersiz kkrdak desteinin sonucunda bronial kollapsn olduu ynnde teoriler de vardr. Sklkla sol st lob, ardndan orta ve sa st loblar etkilenir, alt loblar ise nadiren etkilenir. Olgularn %90 bebeklik dneminde ar solunumsal semptomlarla tan alr. Bu olgu sunumunda, erikin yata tan konan konjenital lober amfizem olgusundan bahsedilecektir.

Anahtar Kelimeler: Konjenital, amfizem, hiperinflasyon

Congenital Lobar Emphysema

Pnar Mutlu, Merve Ilcn Guven
Department of Chest Diseases, anakkale 18 Mart University Faculty of Medicine, anakkale, Turkey

Congenital lobar emphysema is defined by hyperinflation of 1 or more lung lobes in the absence of extrinsic bronchial obstruction. It is a very rare condition with an incidence of 1 in 20,000 to 30,000 births. The etiology is unknown in 50% of cases. Other factors suspected in the etiology are bronchial abnormalities or alveolar defects. Some theories also include bronchial collapse as a result of insufficient cartilage support. The left upper lobe is frequently affected, followed by the middle and right upper lobes, while the lower lobes are rarely affected. Some 90% of cases are diagnosed in infancy with severe respiratory symptoms. In this report, a case of congenital lobar emphysema diagnosed in adulthood is described.

Keywords: Congenital, emphysema, hyperinflation

Olgunun Grnt Kesitleri




Pnar Mutlu, Merve Ilcn Guven. Congenital Lobar Emphysema. Respir Case Rep. 2018; 7(1): 50-53

Sorumlu Yazar: Pnar Mutlu, Trkiye
Makale Dili: Trke
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