Respir Case Rep. 2023; 12(3): 119-122 | DOI: 10.5505/respircase.2023.78700

A Rare Cause of Mediastinal Lymphadenomegaly: Rosai-Dorfman-Destombes Disease

Atilla Can¹, Hüseyin Yýldýran¹, Halil Þen¹, Güven Sadi Sunam², Pýnar Karabaðlý^3
1Department of Thoracic Surgery, Selçuk University School of Me-dicine, Konya, Türkiye
²Thoracic Surgeon, Ýstanbul, Türkiye
³Department of Pathology, Selçuk University School of Medicine, Konya, Türkiye

Rosai-Dorfman-Destombes disease (RDD) is a rare condition that typically presents with cervical lymphadenopathy. The disease usually follows a benign clinical course, and its occurrence in mediastinal lymph nodes is extremely rare. We present here a 48-year-old female patient with Rosai-Dorfman-Destombes disease that manifested as mediastinal lymphadenomegaly, and who was diagnosed by mediastinoscopy.

Keywords: Mediastinal lymphadenomegaly, mediasti-noscopy, Rosai-Dorfman-Destombes disease.

---

Mediastinal Lenfadenomegalinin Nadir Bir Nedeni: Rosai-Dorfman-Destombes Hastalýðý

Atilla Can¹, Hüseyin Yýldýran¹, Halil Þen¹, Güven Sadi Sunam², Pýnar Karabaðlý^3
1Selçuk Üniversitesi Týp Fakültesi, Göðüs Cerrahisi Ana Bilim Dalý, Konya
²Göðüs Cerrahisi Uzmaný, Ýstanbul
³Selçuk Üniversitesi Týp Fakültesi, Patoloji Ana Bilim Dalý, Konya

Rosai-Dorfman-Destombes hastalýðý (RDDH), tipik olarak servikal lenfadenopati ile kendini gösteren nadir bir hastalýktýr. Hastalýk genellikle iyi huylu bir klinik seyir gösterir. Mediastinal lenf nodlarýnda görülmesi son derece nadirdir. Bu yazýda 48 yaþýnda kadýn hastada mediastinal lenfadenomegali þeklinde ortaya çýkan ve mediastinoskopi ile tanýsý konulan Rosai Dorfman Destombes hastalýðý olgusunu sunu-yoruz.

Anahtar Kelimeler: Mediastinal lenfadenomegali, mediastinoskopi, Rosai-Dorfman-Destombes hastalýðý.

---

Image Slices of the Case

---

CITE