e-ISSN 2147-2475

Hzl Arama




Laparoscopic Endoscopic Surgical Science Konnektif Doku Hastal ve ALCAPA Sendromu olan Bir Hastada Pulmoner Arteriyal Hipertansiyon [Respir Case Rep]
Respir Case Rep. 2021; 10(2): 92-94 | DOI: 10.5505/respircase.2021.45722

Konnektif Doku Hastal ve ALCAPA Sendromu olan Bir Hastada Pulmoner Arteriyal Hipertansiyon

Wang Kin Wong1, Wan-Jing Ho2, Jaw-Ji Chu3, Shue-Fen Luo4
1Chang Gung niversitesi Tp Fakltesi, Chang Gung Memorial Hastanesi, Tao-Yuan, Tayvan
2Chang Gung niversitesi, Chang Gung Memorial Hastanesi, Kardiyoloji Blm, Tao-Yuan, Tayvan
3Department of Cardiothoracic and Vascular Surgery, Chang Gung Memorial Hospital, Chang Gung Universi-ty, Tao-Yuan, Taiwan
4Chang Gung niversitesi, Chang Gung Memorial Hastanesi, Romatoloji, Allerji ve mmnoloji Blm, Tao-Yuan, Tayvan

Mikst konnektif doku hastal olan 43 yandaki kadnda, pulmoner arteriyel hipertansiyon aratrmalar srasnda, yaayan bir yetikinde, pulmoner arterden orijin alan sol koroner arter anomalisi saptand. Konjenital anomalinin cerrahi tedavisi ncesi ve sonras, ciddi pulmoner hipertansiyon ynetim stratejisini aklyoruz.

Anahtar Kelimeler: Pulmoner arteriyal hipertansiyon, pulmoner hipertansiyon, pulmoner arterden kaynak-lanan sol koroner arter anomalisi, ALCAPA, konnektif doku hastal.

Pulmonary Arterial Hypertension in a Patient with Connective Tissue Disease and ALCAPA Syndrome

Wang Kin Wong1, Wan-Jing Ho2, Jaw-Ji Chu3, Shue-Fen Luo4
1School of Medicine, Chang Gung University, Chang Gung Memorial Hospital, Tao-Yuan, Taiwan
2Department of Cardiology, Chang Gung Memorial Hospital, Chang Gung University, Tao-Yuan, Taiwan
3Chang Gung niversitesi, Chang Gung Memorial Hastanesi, Kardiotorasik ve Vaskler Cerrahi Blm, Tao-Yuan, Tayvan
4Department of Rheumatology, Allergy and Immunolo-gy, Chang Gung Memorial Hospital, Chang Gung Uni-versity, Tao-Yuan, Taiwan

A 43-year-old female with mixed connective tissue disease was incidentally discovered to be an adult survivor of an anomalous left coronary artery originating from the pulmonary artery during a work-up for her pulmonary hypertension. We describe here the management strategy of severe pulmonary hypertension prior to and after the surgical correction of the congenital anomaly.

Keywords: Pulmonary hypertension, pulmonary arterial hypertension, anomalous left coronary ar-tery originating from the pulmonary artery, ALCAPA, connective tissue disease.







Wang Kin Wong, Wan-Jing Ho, Jaw-Ji Chu, Shue-Fen Luo. Pulmonary Arterial Hypertension in a Patient with Connective Tissue Disease and ALCAPA Syndrome. Respir Case Rep. 2021; 10(2): 92-94

Sorumlu Yazar: Wan-Jing Ho, Taiwan
LookUs & Online Makale